Management
Guidelines
Portal
DNDF Model
VLCAD Nutrition Management Guidelines
First Edition
February 2019, v.1.0
Updated: February 2019
Feedback/Comments
Send us your Feedback & Comments
Overview
Nutrition Guidelines Project

The Nutrition Management Guideline for individuals with very-long-chain acyl-CoA dehydrogenase deficiency (VLCAD) is part of a larger project undertaken by the Southeast Regional Genetics Network (SERN) (HRSA Region 3) and Genetic Metabolic Dietitians International (GMDI) to develop nutrition management guidelines for inherited metabolic disorders (IMD).

Purpose

The purpose of this guideline is to foster optimum nutrition management of individuals with VLCAD and reduce the uncertainty and variability in the management of this IMD.

Target Population

The target population includes individuals with VLCAD at all life stages from the newborn period, through childhood and adolescence, to management in the adult years and during pregnancy. These guidelines include management during periods of health and illness.

Intended Users of the Guidelines

The guidelines are intended for use by metabolic dietitians, physicians, others of the health care team and researchers who collaborate to provide care and advice for individuals with VLCAD as well as their families, advocates, and others.

Sponsor Organization

Sponsorship is shared by SERN and GMDI.

Funding

Funding for this project has been provided by Health Resources and Services Administration (HRSA) grant number: #UH7MC30772 and GMDI.

Content Highlights
  • Methodology used for development of evidence and consensus-based guidelines
  • Background information about VLCAD, its diagnosis, biochemical pathway and nutrition treatment rationale
  • Nutrition care in VLCAD, including assessment, nutrition problem identification, nutrition intervention with evidence- and consensus-based recommendations, and monitoring and evaluation
  • Specific recommendations with ratings based on the strength of the evidence
  • Consideration for implementation
  • Direction for future research
© 2006-2015   —   SOUTHEAST REGIONAL GENETICS NETWORK   —   A HRSA SUPPORTED PARTNERSHIP   —   GRANT #UH7MC30772